Table of Contents page: Journal of Cystic Fibrosis

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Editorial Board

Published in issue: May 2022

ii

News article

Published in issue: May 2022

p379-380

The sweat chloride test has lived up to the changes in CF care

Tanja Gonska

Published in issue: May 2022

p381-382

A new era has dawned for persons with cystic fibrosis; however many knowledge gaps exist in our efforts to improve care

Denis Hadjiliadis,
Emily Siu Clausen

Published online: April 16, 2022

p383-384

Constipation and cystic fibrosis. Slow movement

H.P.J. van der Doef,
R.H.J. Houwen

Published online: April 12, 2022

p385-386

Pregnancy in cystic fibrosis: Review of the literature and expert recommendations

Raksha Jain,
Traci M. Kazmerski,
Lisa C. Zuckerwise,
...
Jacqui Sjoberg,
Madeline Poranski,
Jennifer L. Taylor-Cousar

Published online: August 26, 2021

p387-395

Open Access

How the sweat gland reveals levels of CFTR activity

Jeffrey J. Wine

Published online: February 17, 2022

p396-406

Open Access

Needle-free iontophoresis-driven β-adrenergic sweat rate test

Audrey Reynaerts,
François Vermeulen,
Angélique Mottais,
...
Raphaël Frédérick,
Rita Vanbever,
Teresinha Leal

Published online: September 03, 2021

p407-415

Sweat testing in the modern era: A national survey of sweat testing practice in the Republic of Ireland

Barrie Maguire,
Ophelia Blake,
Gerard Boran,
...
Caroline Murray,
Basil Elnazir,
Barry Linnane

Published online: October 04, 2021

p416-421

Final results of the southwest German pilot study on cystic fibrosis newborn screening – Evaluation of an IRT/PAP protocol with IRT-dependent safety net

Olaf Sommerburg,
Mirjam Stahl,
Susanne Hämmerling,
...
Andreas E. Kulozik,
Marcus A. Mall,
Georg F. Hoffmann

Published online: November 08, 2021

p422-433

Standards of care guidance for sweat testing; phase two of the ECFS quality improvement programme

N. Cirilli,
K.W. Southern,
J. Barben,
...
NJ Simmonds,
E. De Wachter
on behalf of the ECFS Diagnostic Network Working Group

Published online: January 19, 2022

p434-441

CFTR modulation with elexacaftor-tezacaftor-ivacaftor in people with cystic fibrosis assessed by the β-adrenergic sweat rate assay

Sophia Theres Pallenberg,
Sibylle Junge,
Felix C Ringshausen,
...
Anna Maria Dittrich,
Burkhard Tümmler,
Manuel Nietert

Published online: October 28, 2021

p442-447

Open Access

Reclassifying inconclusive diagnosis after newborn screening for cystic fibrosis. Moving forward

Aurelie Hatton,
Anne Bergougnoux,
Katarzyna Zybert,
...
Caroline Raynal,
Isabelle Sermet-Gaudelus,
Dorota Sands

Published online: December 21, 2021

p448-455

Worldwide rates of diagnosis and effective treatment for cystic fibrosis

Jonathan Guo,
Anna Garratt,
Andrew Hill

Published online: February 03, 2022

p456-462

Open Access

Complete CFTR gene sequencing in 5,058 individuals with cystic fibrosis informs variant-specific treatment

Karen S Raraigh,
Melis A Aksit,
Kurt Hetrick,
...
Ronald L Gibson,
Michael R Knowles,
Garry R Cutting

Published online: November 12, 2021

p463-470

Validation of the French 3-year prognostic score for death or lung transplant in the United States cystic fibrosis population

Kathleen J. Ramos,
Travis Hee Wai,
Jenna Sykes,
...
Siddhartha G. Kapnadak,
Nicole Mayer-Hamblett,
Christopher H. Goss

Published online: August 28, 2021

p471-474

Low body mass index as a barrier to lung transplant in cystic fibrosis

Ann L. Jennerich,
Joseph B. Pryor,
Travis Y. Hee Wai,
...
Moira L. Aitken,
Christopher H. Goss,
Kathleen J. Ramos

Published online: December 15, 2021

p475-481

Outcomes following lung re-transplantation in patients with cystic fibrosis

Ernest G. Chan,
Eric J. Hyzny,
John P. Ryan,
Matthew R. Morrell,
Joseph Pilewski,
Pablo G. Sanchez

Published online: December 20, 2021

p482-488

Sustained effectiveness of elexacaftor-tezacaftor-ivacaftor in lung transplant candidates with cystic fibrosis

Clémence Martin,
Martine Reynaud-Gaubert,
Rebecca Hamidfar,
...
Jean-Louis Paillasseur,
Jennifer Da Silva,
Pierre-Régis Burgel

Published online: February 02, 2022

p489-496

Diagnosing constipation in patients with cystic fibrosis applying ESPGHAN criteria

Marina Abib Stefano,
Natascha Silva Sandy,
Carlos Zagoya,
...
Antonio Fernando Ribeiro,
Jochen G. Mainz,
Elizete Aparecida Lomazi

Published online: September 09, 2021

p497-501

Magnetic resonance imaging of the gastrointestinal tract shows reduced small bowel motility and altered chyme in cystic fibrosis compared to controls

Neele S Dellschaft,
Christabella Ng,
Caroline Hoad,
...
Penny A Gowland,
Giles Major,
Alan R Smyth

Published online: December 15, 2021

p502-505

Intestinal function and transit associate with gut microbiota dysbiosis in cystic fibrosis

Ryan Marsh,
Helen Gavillet,
Liam Hanson,
...
Alan R Smyth,
Damian Rivett,
Christopher van der Gast

Published online: December 08, 2021

p506-513

Open Access

Characteristics of electrolyte imbalance and pseudo-bartter syndrome in hospitalized cystic fibrosis children and adolescents

Danish Abdul Aziz,
Fatima Siddiqui,
Quratulain Abbasi,
Haissan Iftikhar,
Shahira Shahid,
Fatima Mir

Published online: October 02, 2021

p514-518

Cystic fibrosis-related diabetes (CFRD) and cognitive function in adults with cystic fibrosis

Helen K Chadwick,
Janice Abbott,
Margaret Anne Hurley,
...
Clare L Lawton,
Michael W Mansfield,
Daniel Peckham

Published online: June 13, 2021

p519-528

Safety and pharmacokinetics of Roscovitine (Seliciclib) in cystic fibrosis patients chronically infected with Pseudomonas aeruginosa, a randomized, placebo-controlled study

Laurent Meijer,
Geneviève Hery-Arnaud,
Cyril Leven,
...
Gilles Rault,
Dominique Mottier,
Rozenn Le Berre

Published online: December 24, 2021

p529-536

Rescue of chloride and bicarbonate transport by elexacaftor-ivacaftor-tezacaftor in organoid-derived CF intestinal and cholangiocyte monolayers

Marcel J.C. Bijvelds,
Floris J.M. Roos,
Kelly F. Meijsen,
...
Hettie M. Janssens,
Luc J.W. van der Laan,
Hugo R. de Jonge

Published online: December 15, 2021

p537-543

Open Access

Elexacaftor/tezacaftor/ivacaftor for CFTR variants giving rise to diagnostic uncertainty: Personalised medicine or over-medicalisation?

Donatello Salvatore,
Angela Pepe,
Vincenzo Carnovale,
...
Annalisa Amato,
Gianluca Ferrari,
Giuseppe Campagna

Published online: September 25, 2021

p544-548

Ivacaftor withdrawal syndrome: A potentially life-threatening consequence from a life-saving medication

James M. Clegg,
Kelsey W. Malloy,
Rebekah F. Brown,
Alison G. Grisso,
Andrew G. Sokolow

Published online: August 11, 2021

p549-550

Forewarned is forearmed: The cardiovascular time bomb in Cystic Fibrosis

J. Duckers,
R. Fitzgerald,
D. Proud,
C. Addy,
D. Datta

Published online: December 10, 2021

p551-552

Safety of mRNA-based vaccines against SARS-CoV-2 in people with cystic fibrosis aged 12 years and over

Gianfranco Alicandro,
Valeria Daccó,
Lisa Cariani,
...
Andrea Gramegna,
Francesco Blasi,
Carla Colombo

Published online: February 15, 2022

e173-e175

The clinical impact of the Covid-19 pandemic first wave on patients with cystic fibrosis in New York

Joseph L. Simonson,
Christine Esposito,
Theresa Frantzen,
...
Teresa Stables-Carney,
Patricia Walker,
Janice Wang

Published online: February 20, 2022

e176-e183

Immunogenicity of the COVID-19 BNT162b2 vaccine in adolescents and young adults with cystic fibrosis

Athanasios Michos,
Filippos Filippatos,
Elizabeth-Barbara Tatsi,
...
Evgenia Troupi,
Vasiliki Syriopoulou,
Ioanna Loukou

Published online: April 13, 2022

e184-e187

Quality of life is poorly correlated to lung disease severity in school-aged children with cystic fibrosis

Phillip Pattie,
Sarath Ranganathan,
Joanne Harrison,
...
Kathryn Ramsey,
Danielle Wurzel
on behalf of AREST CF

Published online: November 17, 2021

e188-e203

Impact of cross-sensitivity error correction on representative nitrogen-based multiple breath washout data from clinical trials

Paul D. Robinson,
Renee Jensen,
Ryan A. Seeto,
...
Christopher Short,
Jane C. Davies,
Felix Ratjen

Published online: September 12, 2021

e204-e207

Impact of Spiroware re-analysis method on multiple-breath washout outcomes in children with cystic fibrosis

Marc-Alexander Oestreich,
Florian Wyler,
Philipp Latzin,
Kathryn A. Ramsey

Published online: February 26, 2022

e208-e209

Re: Impact of spiroware re-analysis method on multiple-breath washout outcomes in children with cystic fibrosis; M.A. Oestreich, F. Wyler, P. Latzin et al.

Renee Jensen,
Michelle Shaw,
Angel Phanthanourak,
Felix Ratjen

Published online: April 09, 2022

e210-e211

Regarding the articles on home spirometry

Rachael Curley,
Michael J Campbell,
Stephen J Walters,
Zhe Hui Hoo,
Martin J Wildman

Published online: January 15, 2022

e212-e214

Global access to affordable CFTR modulator drugs: Time for action!

Marco Zampoli,
Nataliya Kashirskaya,
Bulent Karadag,
Luiz Vicente Ribeiro Ferreira da Silva Filho,
Grace R. Paul,
Christine Noke

Published online: March 25, 2022

e215-e216

Hypervitaminosis A with fulminant secondary intracranial hypertension following personalized medicine-based Elexacaftor/Tezacaftor/Ivacaftor initiation in a preadolescent with cystic fibrosis

Benjamin L. Wisniewski,
Shawn C. Aylward,
Catherine O. Jordan,
Benjamin T. Kopp,
Grace R. Paul

Published online: February 04, 2022

e217-e220

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