January 2015

Editorial Board
Published in issue: January 2015
ii

Editorial

The growing threat of nontuberculous mycobacteria in CF
• R. Andres Floto,
• Charles S. Haworth
Published online: December 06, 2014
p1-2

News

News
Published online: December 09, 2014
p3-5

Review

Upper aero-digestive contamination by Pseudomonas aeruginosa and implications in Cystic Fibrosis
• R. Rivas Caldas,
• S. Boisramé
Published online: June 02, 2014
p6-15

CFTR/Basic Science

Ibuprofen rescues mutant cystic fibrosis transmembrane conductance regulator trafficking
• Graeme W. Carlile,
• Renaud Robert,
• Julie Goepp,
• ...
• Daniela Rotin,
• John W. Hanrahan,
• David Y. Thomas
Published online: June 25, 2014
p16-25

Stimulation of β_2-adrenergic receptor increases CFTR function and decreases ATP levels in murine hematopoietic stem/progenitor cells
• Teresa Trotta,
• Lorenzo Guerra,
• Donatella Piro,
• ...
• Valeria Casavola,
• Nazzareno Capitanio,
• Massimo Conese
Published online: August 29, 2014
p26-33

Diagnosis/Screening

Function, pharmacological correction and maturation of new Indian CFTR gene mutations
• Himanshu Sharma,
• Mathilde Jollivet Souchet,
• Isabelle Callebaut,
• Rajendra Prasad,
• Frédéric Becq
Published online: July 16, 2014
p34-41

Immunology

Anti-ET_AR and anti-AT₁R autoantibodies are elevated in patients with endstage cystic fibrosis
• K. Budding,
• E.A. van de Graaf,
• T. Hoefnagel,
• ...
• D. Dragun,
• C.E. Hack,
• H.G. Otten
Published online: August 02, 2014
p42-45

Microbiology

Epidemiology of nontuberculous mycobacteria among patients with cystic fibrosis in Scandinavia
• Tavs Qvist,
• Marita Gilljam,
• Bodil Jönsson,
• ...
• Niels Høiby,
• Terese L. Katzenstein
• on behalf of the Scandinavian Cystic Fibrosis Study Consortium (SCFSC)
Published online: August 29, 2014
p46-52

Increasing nontuberculous mycobacteria infection in cystic fibrosis
• Ophir Bar-On,
• Huda Mussaffi,
• Meir Mei-Zahav,
• ...
• Patrick Stafler,
• Shai Hananya,
• Hannah Blau
Published online: June 07, 2014
p53-62

Comparing Mycobacterium massiliense and Mycobacterium abscessus lung infections in cystic fibrosis patients
• Anne-Laure Roux,
• Emilie Catherinot,
• Nathalie Soismier,
• ...
• Didier Guillemot,
• Jean-Louis Gaillard
• for the OMA group
Published online: July 29, 2014
p63-69

Impact of alginate-producing Pseudomonas aeruginosa on alveolar macrophage apoptotic cell clearance
• Charles A. McCaslin,
• Daniela N. Petrusca,
• Christophe Poirier,
• Karina A. Serban,
• Gregory G. Anderson,
• Irina Petrache
Published online: July 11, 2014
p70-77

Pulmonology

Mannose-binding lectin gene as a modifier of the cystic fibrosis phenotype in Argentinean pediatric patients
• Luis Pablo Gravina,
• Carolina Crespo,
• Hilda Giugno,
• ...
• Lilien Chertkoff,
• Andrea Mangano,
• Claudio Castaños
Published online: August 29, 2014
p78-83

Computed tomography correlates with improvement with ivacaftor in cystic fibrosis patients with G551D mutation
• Shahid I. Sheikh,
• Frederick R. Long,
• Karen S. McCoy,
• Terri Johnson,
• Nancy A. Ryan-Wenger,
• Don Hayes Jr.
Published online: July 19, 2014
p84-89

Indicators of pulmonary exacerbation in cystic fibrosis: A Delphi survey of patients and health professionals
• Fiona McCourt,
• Brenda O'Neill,
• Ian Logan,
• ...
• Stephanie McKeown,
• J. Stuart Elborn,
• Judy M. Bradley
Published online: August 12, 2014
p90-96
Central venous thrombosis and thrombophilia in cystic fibrosis: A prospective study
• Anne Munck,
• Ahmed Kheniche,
• Corinne Alberti,
• ...
• Stéphanie Wanin,
• Laurence Weiss,
• Marie-Francoise Hurtaud
Published online: August 05, 2014
p97-103

Survival benefit of induction immunosuppression in cystic fibrosis lung transplant recipients
• Stephen Kirkby,
• Bryan A. Whitson,
• Allison M. Wehr,
• Amy M. Lehman,
• Robert S. Higgins,
• Don Hayes Jr.
Published online: June 16, 2014
p104-110

Clinical Trials

Open label study of inhaled aztreonam for Pseudomonas eradication in children with cystic fibrosis: The ALPINE study
• H.A.W.M. Tiddens,
• K. De Boeck,
• J.P. Clancy,
• ...
• S.A. Lewis,
• C.M. Oermann
• for the ALPINE study investigators
Published online: August 01, 2014
p111-119

Nutrition/Gastroenterology

Outcome in patients with cystic fibrosis liver disease
• Marion Rowland,
• Cliona Gallagher,
• Charles G. Gallagher,
• ...
• Leslie Daly,
• Noel G. McElvaney,
• Billy Bourke
Published online: June 07, 2014
p120-126

Endocrinology

Cystic fibrosis-related bone disease explored using a four step algorithm
• Denise S.K. Brookes,
• Julie N. Briody,
• Craig F. Munns,
• Peter S.W. Davies,
• Rebecca J. Hill
Published online: August 26, 2014
p127-134

Disposition index identifies defective beta-cell function in cystic fibrosis subjects with normal glucose tolerance
• L. Merjaneh,
• Q. He,
• Q. Long,
• L.S. Phillips,
• A.A. Stecenko
Published online: July 03, 2014
p135-141

Psychosocial

Opportunities for cystic fibrosis care teams to support treatment adherence
• Kristin A. Riekert,
• Michelle N. Eakin,
• Andrew Bilderback,
• Alana K. Ridge,
• Bruce C. Marshall
Published online: October 24, 2014
p142-148

Book Review

• Patrick Flume
Published in issue: January 2015
p149

Letters to the Editor

Raw meat contaminated with epidemic clones of Burkholderia multivorans found in cystic fibrosis patients
• Agnese Lupo,
• Enver Isis,
• Vincent Perreten,
• Andrea Endimiani
Published online: July 24, 2014
p150-152
Pancreatic enzymes and Fibrosing Colonopathy
• John A. Dodge
Published online: September 18, 2014
p153
Use of neutrophil gelatinase-associated lipocalin (NGAL) in CF
• Courtney Munro,
• Sarath Ranganathan,
• Kingsley Coulthard,
• Cathy Quinlan
Published online: July 10, 2014
p154
What is hepcidin telling us about the natural history of cystic fibrosis?
• A.H. Gifford
Published online: April 30, 2014
p155-157
Regarding the article entitled “Iron supplementation does not worsen respiratory health or alter the sputum microbiome in cystic fibrosis”
• Z.H. Hoo,
• M.J. Wildman
Published online: June 24, 2014
p158-159

Corrigendum

Corrigendum to “Prescribing practices for intravenous aminoglycosides in UK Cystic Fibrosis clinics: A questionnaire survey” [J Cyst Fibros (2013) 424-427]
• Alan R. Smyth,
• Emma L. Campbell
Published online: September 18, 2014
p160