- •Pseudo-Bartter syndrome (PBS) can be a presenting feature of cystic fibrosis in children.
- •Polyuria was most common in the PBS (72%) group.
- •Normal ranges of renin and aldosterone and urinary electrolytes are in consistent with the diagnosis of PBS secondary to CF.
- •Gastrointestinal presentations including diarrhea, vomiting and constipation were more common in patients with the Electrolyte imbalance (EI) and PBS groups.
- •Pseudomonas colonization is less frequent in patients presenting with PBS.
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