Journal of Cystic Fibrosis
Volume 9, Issue 4 , Pages 246-249, July 2010

Pneumothorax in cystic fibrosis: Prevalence and outcomes in Scotland

  • A. MacDuff

      Affiliations

    • Department of Respiratory Medicine, Western General Hospital, Crewe Road South, Edinburgh, EH4 2XU, United Kingdom
    • Corresponding Author InformationCorresponding author. Tel.: +44 1896 826000.
    • ,
  • J. Tweedie

      Affiliations

    • Department of Medicine, Western Infirmary, Dumbarton Road, Glasgow, G11 6NT, United Kingdom
    • ,
  • L. McIntosh

      Affiliations

    • Department of Respiratory Medicine, Western General Hospital, Crewe Road South, Edinburgh, EH4 2XU, United Kingdom
    • ,
  • J.A. Innes

      Affiliations

    • Department of Respiratory Medicine, Western General Hospital, Crewe Road South, Edinburgh, EH4 2XU, United Kingdom

Received 27 January 2010; received in revised form 28 March 2010; accepted 20 April 2010.

Abstract 

Background

Pneumothorax is a feared complication of cystic fibrosis. With improved survival into adult life the incidence of pneumothorax is expected to increase. The optimal management of these patients is unclear.

Methods

Case review of patients from the three Scottish adult CF centres.

Results

A total of 22 episodes of pneumothorax occurred in 20 patients over a 12year period. 2 patients died as a result of the pneumothorax. 16 pneumothoraces were treated by insertion of an intercostal drain and 8 by observation. 8 patients suffered a prolonged air leak. 5 patients were treated with pleurodesis. Pneumothorax was associated with a small decline in lung function which persisted for at least 1year.

Conclusion

Pneumothorax can present a challenge to treat in adult CF. However successful outcomes can be achieved even in cases of prolonged air leaks. Current national guidelines help in selecting optimal pleural interventions.

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PII: S1569-1993(10)00062-7

doi:10.1016/j.jcf.2010.04.005

Journal of Cystic Fibrosis
Volume 9, Issue 4 , Pages 246-249, July 2010

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